Fibrosarcoma Of The Lower Extremity Of The Femur (About A Case)
A.Chagou, A.Rhanim, R.Zanati, A Bardouni, M.Mahfoud, MS Berrada, M,Yaacoubi.
Key words: amputation, bone, biopsy, chemotherapy, fibro sarcoma, prognosis.
Abstract: Case report: Primitive bone fibro sarcoma is a rare entity; it is only 3-5% of malignant tumours of the bone. We report the case of a 24 years old patient without significant history, having consulted for pain in the left thigh accented night with impaired general condition. Surgical biopsy revealed a low-grade fibro sarcoma of malignancy. The treatment consisted of a trans femoral amputation. The short-term trend (12 months) is good, with no local recurrence and amputation stump clean. Discussion: Primitive bone fibro sarcoma is a rare entity; it is dominant between 40 and 60 years. The femur and tibia are the predilection, Radiographs highlight an image of osteolysis, periosteal reaction is inconstant and invasion of soft tissues is possible. Treatment is mainly surgical; it typically consists of a limb amputation. Several chemotherapy protocols are proposed, but none has shown consistent efficacy, the prognosis remains reserved.
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